From: Hypoketotic hypoglycemia in citrin deficiency: a case report
Laboratory Measure | Pre-starvation test | Post-starvation hour | Post-intake hour | 2 | |||
---|---|---|---|---|---|---|---|
10 | 12 | 13 | 0.5 | 1 | |||
Blood glucose, mM | 4.17 | 3.44 | 1.89 | 5.67 | 7.28 | 7.78 | |
Lactate, mM | 5.40a | 1.98 | 1.63 | 1.36 | 1.41 | ||
Pyruvate, mM | 0.10 | 0.10 | 0.09 | 0.13 | |||
Acetoacetic acid, μM | 40 | 576 | 784 | 820 | 411 | ||
β-Hydroxybutyrate, μM | 67 | 300a | 1616 | 1551 | 1582 | 646 | |
Total ketone bodies, μM | 107 | 2192 | 2335 | 2402 | 1057 | ||
Free fatty acid, mM | 4.4 | 2.5 |